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Current Pediatric Research| Volume: 22
November 28-29, 2018 | Dubai, UAE
15th World Congress on
Pediatrics, Clinical Pediatrics and Nutrition
28th International Conference on
Nursing Practice
Joint Event
&
The Limbal Dermoid in Goldenhar Syndrome are usually
unilateral. Although they rarely can be bilateral. They either
involve the entire cornea ormay be confined to conjunctiva only
the commonest site 70 percent of infero temporal incidence is
1 in 10, 000 or 1 in 500 to 2, 700 They are graded according to
corneal involvement.
a. Grade1 is corneal epithelial involvement
b. Grade2 is des membrane involvement
c. Grade3 is entire anterior segment involvement
Case Report: 9 months back a 3 years male child was seen by
me in my office with parents having noticed a very small polish
white infero temporal limbal opacity in left eye. Since birth with
associated congenital presence of a pre-auricular appendage
on right side. There were no other congenital anomalies.
First child delivered after l second is no history of exposure to
oxygen, jaundice, breast fed normal mile stones with normal
intelligence. MRI (Magnetic Resonance Imaging) orbits did not
show underlying orbital involvement, normal hearing, a teeth,
ear, normal spine, limbs, kidney and vision. Anterior Segment
Refraction functioning was normal. So, the child had grade l
dermoid which begin at the commonest site of infero temporal
site.
Discussion: Goldenhar Syndrome has a very good prognosis.
Most of the children live normally with normal vision. Only 5 to
15 percent may have other congenital anomalies.
Conclusion: One should reassure the parent about this disorder
which in majority of children is not visual threatening. However,
if the limbal dermoid involves visual axis and their tens vision
then we have following surgical modalities as visual and
cosmotic. The surgical procedures are Lamellar Keratoplasty,
Amniotic membrane graft and Stem cell graft.
1. There are many Goldenhars Syndrome support groups.
2. Families of Goldenhars Syndrome are seen. 17 such families
of Goldenhar Syndrome are seen in Greece.
3. Mittal Et al Indian Journal of Ophthalmology, 1968 reported
3 case of optic nerve drusen’s associated with goldenhars
Syndrome.
4. Infants born in Middle East in Gulf War in different military
hospital were reported to have Goldenhars Syndrome.
5. In cases of Goldenhar Syndrome with associated hare lip,
cleft palate, pre-auricular appendage or skin tag, plastic surgical
intervention is needed.
Speaker Biography
Gowhar Ahmad is a Director in the Department of Ophthalmology, Florence
Hospital, Multispeciality Center, Kashmir, India. He completed his Master’s in
Surgery from University of Agra, India in the year 1976. He obtains fellowship in
Paediatric Ophthalmology from Morefield’s Eye Hospital, London and in Oculoplaty
and Neurophthalmology from King Khaled Eye Specialist Hospital, Riyadh. Saudi
Arabia. He had more than 40 years of experience in field of Ophthalmology
with guest National and International speakers. He has posted more than 6oo
Ophthalmic articles on Linked-in, 700 on Docpleuxs and more than 1400 on
Curofy. He has many International publications. He served as Editorial Member
for International Journal of Science and Research. His main field of interest is
Paediatric Ophthalmology, Oculoplaty and Neurophthalmology. His is also interested
in community ophthalmology and has conducted many eye camps in rural areas.
e:
Rare and Interesting case of Goldenhars Syndrome in a 3 years male child
Gowhar Ahmad
University of Jammu and Kashmir, India
Gowhar Ahmad, Pediatrics and Clinical Pediatrics 2018
& Nursing Practice 2018, Volume 22
DOI: 10.4066/0971-9032-C2-005