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September 20-22, 2017 | Toronto, Canada

AMERICAN PEDIATRICS HEALTHCARE &

PEDIATRIC INFECTIOUS DISEASES CONGRESS

Pediatric Healthcare & Pediatric Infections 2017

yke-Davidoff-Masson syndrome (DDMS) was described initially by C G

Dyke, L M Davidoff and C B Masson in 1933. It results from an insult

to the growing brain in utero or early infancy, leading to loss of neurons,

compromising the growth of the brain. Diagnosis is established with clinical

and neuroimaging data. Patients may require physiotherapy, speech and

occupational therapy in addition to the management of the seizures.

Awareness among the pediatrician, the radiologist and the team leads to

early recognition, appropriate timely management and hence, better long-

term prognosis. A nine years old female born prematurely, presented thrice

in her lifetime as a case of status epilepticus due to improper and inadequate

use of prescribed medications. She had delayed mental development for

her age. Upon contrast, CT evaluation, hemiatrophy of the right cerebral

hemisphere with compensatory ex-vacuo ventriculomegaly and midline

shift towards the right, ipsilateral thickening of the calvarium, decrease in

size of the ipsilateral cranial fossa, unilateral overdevelopment of the frontal

sinus and overaerated right petrous were noted. Capillary malformation

was seen as spoke-wheel appearance of the capillaries in the right basal

ganglia, a novel finding in children with DDMS. She was diagnosed as a case

of DDMS and was managed with IV and oral anticonvulsants and advised

for the behavioral therapy to follow on out-patient basis. Neurosurgical

consultation was also advised in case of intractable seizures for possible

hemispherectomy, which has a success rate of 85% in selected cases. DDMS

is a rare clinical entity and furthermore, status epilepticus is an unusual

presenting complaint. The physicians must be aware of this relatively

uncommon clinical presentation of status epilepticus in order for a timely

and appropriate management and also for the outcome of a better long-

term prognosis.

Speaker Biography

Ghimire Pradesh has completed his MBBS from Manipal College of Medical Sciences

affiliated to Kathmandu University, Nepal. He is a third year Radiology Resident in Bicol

Medical Center affliliated to Bicol University, Philippines.

A rare entity with a rarer presentation: A case report on Dyke-Davidoff Masson syndrome presenting

with status epilepticus

Pradesh Ghimire, Collao M and Bista N

Bicol Medical Center, Philippines