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alliedacademies
August 16-17, 2018 | Paris, France
Primary Healthcare
12th International Conference on International Conference and Medicare Expo on
&
Pediatrics Health Care
Joint Event
Journal of Current Pediatric Research | Volume: 22
Congenital Pulmonary Airway Malformation (CPAM): A case series; Radiographic importance in
diagnosis
Pradesh Ghimire
Bicol Medical Center, Philippines
Congenital Pulmonary Airway Malformation (CPAM) is a
rare (1-4/100,000 births) congenital anomaly, with male
predominance (95% cases), presenting as a multi-cystic mass
of segmental lung tissue with abnormal bronchial proliferation;
considered as a part of the spectrum of Broncho-pulmonary
foregut malformations. It is believed to be a result of arrested
development of the fetal bronchial tree during sixth and
seventh week of fetal development. Thyroid transcription
factor 1 defect is also considered a possibility. Malignancy and
frequent airway infections aremajor concerns in these patients.
Surgical excision is recommended to make a definite diagnosis,
to exclude hidden malignancies, and is also the treatment of
choice.
Herein, I report a three cases series of different types of
Congenital Pulmonary Airway Malformation (CPAM); all
presenting with infection. Two of them (2 month and 2 year old
males respectively) who were diagnosed as type IV presented
with a clinical diagnosis of large pleural effusion. Secondary post
chest tube drainage, they were diagnosed (using radiographic
and CT scan correlation) with localized large multi-cystic
radiolucency’s in the right lung field with significant midline
shift on chest radiography. The third case is of a 3 month old
female; being a type II, who presented with empyema thoracis.
Contrast CT aided in the diagnosis of multiple small cystic
changes in the lungs. All these cases were managed in pediatric
ICU and pediatric surgery services.The recent trend of antenatal
detection using MRI and ultrasound as well as management, to
some extent has tremendously improved the life expectancy of
such cases. However, availability of timely diagnosis, necessary
radio-imagining modalities and appropriate management still
are quite a challenge in the developing countries.
Speaker Biography
Pradesh Ghimire has completed his MBBS from Manipal College of Medical Sciences
affiliated to Kathmandu University, Nepal. He is a fourth year radiology resident in Bicol
Medical Center, Naga city, Philippines.
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Notes:
Pradesh Ghimire, Pediatrics & Primary HealthCare 2018, Volume 22
DOI: 10.4066/0971-9032-C1-002